The clinical practice guideline on diagnosis of idiopathic pulmonary fibrosis (IPF) by Raghu and colleagues has been helpful in addressing the complexities of radiological and pathological features in diagnosing IPF. The heterogeneity of features and limited understanding of the pathogenesis and progression of fibrotic lung disease as well as the option of antifibrotic therapy have made this a timely article. The latest iteration has reduced the number of diagnostic subtypes to three groups: IPF, probable IPF, and uncertain IPF. In previous studies, the presence of reticulation and traction bronchiectasis without GGO (previous possible IPF) usually yielded a UIP pathological diagnosis and a final diagnosis of IPF.

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